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Valve-Sparing Replacement of the Aortic Root for a 2-year-old Child with Loeys-Dietz Syndrome

Published online by Cambridge University Press:  23 October 2009

Yoshio Ootaki ,
Minhaz Uddin  and
Ross M. Ungerleider
Yoshio Ootaki
Affiliation:
Division of Pediatric Cardiothoracic Surgery, Rainbow Babies and Children’s Hospital, University Hospitals Case Medical Center, Cleveland, Ohio, USA
Minhaz Uddin
Affiliation:
Division of Pediatric Cardiothoracic Surgery, Rainbow Babies and Children’s Hospital, University Hospitals Case Medical Center, Cleveland, Ohio, USA
Ross M. Ungerleider*
Affiliation:
Division of Pediatric Cardiothoracic Surgery, Rainbow Babies and Children’s Hospital, University Hospitals Case Medical Center, Cleveland, Ohio, USA
*
Correspondence to: Dr Ross Ungerleider, 11100 Euclid Avenue, Cleveland, OH 44106, USA. Tel: 216-844-3058; Fax: 216-844-3517; E-mail: ross.ungerleider@UHhospitals.org
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Abstract

Loeys-Dietz syndrome is a newly recognized constellation that presents with aortic aneurysm or dissection similar to Marfan’s syndrome. We describe successful surgical treatment in a 2-year-old with the syndrome in whom we performed a valve-sparing replacement of the aortic root because of significant dilation of the aortic root and the ascending aorta.

Keywords

Genetic syndromeaortic root dilationascending aortic aneurysm
Type
Brief Reports
Information
Cardiology in the Young , Volume 20 , Issue 1 , February 2010 , pp. 94 - 96
Copyright
Copyright © Cambridge University Press 2009

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References

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