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Double epiglottis in Weyer's acrofacial dysostosis

Published online by Cambridge University Press:  29 June 2007

F. J. Wittig ,
S. A. Hickey  and
M. Kumar
F. J. Wittig
Affiliation:
Department of Otorhinolarngology, Torbay Hospital, Torquay, U.K.
S. A. Hickey*
Affiliation:
Department of Otorhinolarngology, Torbay Hospital, Torquay, U.K.
M. Kumar
Affiliation:
Department of Otorhinolarngology, Torbay Hospital, Torquay, U.K.
*
Address for correspondence: Mr. S. A. Hickey, Torbay Hospital, Lawes Bridge, TorquayTQ2 7AA. Fax: 01803 65 4898
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Abstract

While evaluating a 61-year-old patient for stridor we incidentally detected a double epiglottis. The patient was also diagnosed of having Weyer's acrofacial dysostosis which is characterized by hexadactyly affecting all four extremities, small and deeply set nails, dental deformities with small, conical teeth and mandibular hypoplasia. The double epiglottis was not the cause for the stridor. Because of the covert symptomatology of double epiglottis it is suggested that the association with Weyer's syndrome is common. Embryological evidence and a review of the literature on laryngeal abnormalities is discussed.

Keywords

EpiglottisCongenital defects
Type
Clinical Records
Information
The Journal of Laryngology & Otology , Volume 112 , Issue 10 , October 1998 , pp. 976 - 978
Copyright
Copyright © JLO (1984) Limited 1998

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