Cardiology in the Young

Review Articles

Intramuscular small vessel arteriovenous malformation of the left ventricle in an asymptomatic adolescent: a case report and literature review

Amy N. McCammonda1 c1, Erin R. Rudzinskia2, Brian J. Morrisona3 and Michael Silberbacha3

a1 Department of Pediatrics, Division of Pediatric Cardiology, Lucile Packard Children's Hospital at Stanford, Palo Alto, California, United States of America

a2 Department of Pathology, Oregon Health & Science University, Portland, Oregon, United States of America

a3 Department of Pediatrics, Division of Pediatric Cardiology, Doernbecher Children's Hospital, Portland, Oregon, United States of America

Abstract

Primary vascular tumours of the heart are rare and heterogeneous in their presentation and classification. We present a primary intramuscular vascular malformation of the left ventricle in an asymptomatic 12-year-old girl. Characteristics on cardiac magnetic resonance imaging, specifically increased signal intensity on T2-weighted images, and marked contrast enhancement with gadolinium were suggestive of increased vascularity. Histologically, the mass was determined to be an intramuscular vascular malformation of the small vessel arteriovenous subtype. This represents one of a select few intramuscular vascular malformations of the left ventricle reported in children. Our patient remains completely asymptomatic and has had no change in the size and appearance of the mass after more than 30 months of follow-up.

(Received March 03 2012)

(Accepted February 24 2013)

(Online publication May 22 2013)

Keywords

  • Cardiac tumours;
  • heart-vascular neoplasms;
  • vascular anomalies;
  • arteriovenous

Correspondence

c1 Correspondence to: Dr A. N. McCammond, MD, Department of Pediatrics, Division of Pediatric Cardiology, Lucile Packard Children's Hospital at Stanford, 750 Welch Road, Suite 325., Palo Alto, California 94304, United States of America. Tel: +650 723 7913; Fax: +650 723 8343; E-mail: amym1@stanford.edu

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