Cardiology in the Young

Brief Reports

Systemic hypertension in an infant with unrepaired tetralogy of Fallot: case report

Michael Khourya1, Michael Kallilea2, Joseph Maya2 and Rajesh Punna2 c1

a1 Department of Paediatrics, The Hospital for Sick Children, Toronto, Ontario, Canada

a2 Division of Pediatric Cardiology, Lucile Packard Children's Hospital, Palo Alto, CA, United States of America

Abstract

Patients with severe right ventricular outflow tract obstruction in tetralogy of Fallot typically have right-to-left shunting, resulting in low pulmonary blood flow and cyanosis. Here we present the case of an infant with tetralogy of Fallot and severe pulmonary valve stenosis, complicated by systemic hypertension, the presence of which altered flow dynamics and possibly prevented cyanosis.

(Received June 20 2012)

(Accepted September 22 2012)

(Online publication November 13 2012)

Keywords

  • Tetralogy of fallot;
  • hypertension;
  • systemic vascular resistance

Correspondence

c1 Correspondence to: Dr R. Punn, MD, Division of Pediatric Cardiology, Lucile Packard Children's Hospital, 750 Welch Road, Suite no. 305, Palo Alto, CA 94304, United States of America. Tel: +1 650 498 4563; Fax: +1 650 725 8343; E-mail: rpunn@stanford.edu