The Journal of Laryngology & Otology

Clinical Records

A rare angiosarcoma: retiform haemangioendothelioma

F O'Duffya1 c1, C Timona1 and M Tonera2

a1 Department of Otorhinolaryngology, Royal Victoria Eye and Ear Hospital, Dublin, Ireland

a2 Department of Pathology, St James's Hospital, Dublin, Ireland

Abstract

Objective: We report the case of a rare angiosarcoma, retiform haemangioendothelioma, in an 18-year-old young man, which presented as a recurrent ulcerating lesion of the left pinna.

Method: Case report and literature review of retiform haemangioendothelioma. This is a low grade angiosarcoma with a high local recurrence rate and low metastasis rate, and was first described in 1994 by Calonje et al.

Results: This patient represents only the third report of lymph node metastasis in a case of retiform haemangioendothelioma. To date, 31 cases of the tumour have been reported. Histological diagnosis of this group of vascular neoplasms can be challenging, as their histopathological appearance is intermediate between haemangioma and angiosarcoma.

Conclusion: Surgical excision remains the primary treatment modality, with adjuvant radiotherapy recommended in patients with large tumour size, local recurrence and lymph node metastasis, as seen in this case.

(Accepted April 21 2011)

(Online publication September 05 2011)

Correspondence:

c1 Address for correspondence: Mr Fergal O'Duffy, Royal Victoria Hospital, Adelaide Rd, Dublin 2, Ireland Fax: +353 14900643 E-mail: fergaloduffy@hotmail.com

Mr F O'Duffy takes responsibility for the integrity of the content of the paper

Competing interests: None declared