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Feeding, growth, nutrition, and optimal interstage surveillance for infants with hypoplastic left heart syndrome

Published online by Cambridge University Press:  13 December 2011

David A. Hehir ,
David S. Cooper ,
Elizabeth M. Walters  and
Nancy S. Ghanayem
David A. Hehir*
Affiliation:
Division of Pediatric Cardiology, Children's Hospital of Wisconsin and Medical College of Wisconsin, Milwaukee, Wisconsin, United States of America Division of Pediatric Critical Care Medicine, Children's Hospital of Wisconsin and Medical College of Wisconsin, Milwaukee, Wisconsin, United States of America
David S. Cooper
Affiliation:
The Heart Institute, Cincinnati Children's Hospital Medical Center, University of Cincinnati College of Medicine, Cincinnati, Ohio, United States of America
Elizabeth M. Walters
Affiliation:
The Heart Center, All Children's Hospital, Miami, Florida, United States of America
Nancy S. Ghanayem
Affiliation:
Division of Pediatric Critical Care Medicine, Children's Hospital of Wisconsin and Medical College of Wisconsin, Milwaukee, Wisconsin, United States of America
*
Correspondence to: Dr D. A. Hehir, MD, 9000 West Wisconsin Avenue, Milwaukee, Wisconsin 53201, United States of America. Tel: 414-266-5711; Fax: 414-266-3563; E-mail: dhehir@mcw.edu
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Abstract

Improvement in operative survival of patients with hypoplastic left heart syndrome has led to increasing emphasis on prevention of interstage mortality. Many centres have improved interstage results through programmes of home monitoring following discharge after the Norwood (Stage 1) operation. Experience with heightened interstage surveillance has identified failure to thrive during infancy as a modifiable risk factor for this population, one that has been linked to concerning outcomes at subsequent palliative surgeries. Ensuring normal growth as an infant has thus become a priority of management of patients with functionally univentricular hearts. Herein, we review the existing evidence for best practices in interstage surveillance and optimal nutrition in infants with functionally univentricular hearts. In addition, we highlight data presented at HeartWeek 2011, from Cardiology 2011, the 15th Annual Update on Pediatric and Congenital Cardiovascular Disease, and the 11th Annual International Symposium on Congenital Heart Disease.

Keywords

Hypoplastic left heart syndromecongenital cardiac diseasegrowth
Type
Original Article
Information
Cardiology in the Young , Volume 21 , Issue S2: A Holistic Approach to Hypoplastic Left Heart Syndrome and other evolving challenges in Pediatric and Congenital Cardiac Disease , 13 December 2011 , pp. 59 - 64
Copyright
Copyright © Cambridge University Press 2011

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