a1 Department of Otolaryngology, Stanford University, California, USA
a2 Department of Pathology, Stanford University, California, USA
Objective: To review the existing diagnostic modalities and treatment for primary tracheal synovial sarcoma, and to report a case of primary cervical synovial sarcoma arising in the trachea.
Setting: Head and neck surgery unit at a tertiary university centre.
Patient: One case of primary cervical tracheal monophasic synovial sarcoma diagnosed by SYT–SSX gene rearrangement.
Intervention: This patient underwent surgical resection of the synovial sarcoma, together with tracheal resection and primary anastomosis assisted by laryngeal-releasing manoeuvres, without complication.
Main outcome measures: Clinical, radiographical, pathological and surgical information were collected.
Result: One year post-operatively, there was no evidence of recurrence.
Conclusion: Synovial sarcoma arising in the trachea is very rare. Diagnosis is confirmed by demonstrating the SYT–SSX gene rearrangement. The first-line treatment is surgery.
(Accepted August 24 2010)
(Online publication January 31 2011)
Dr E J Damrose takes responsibility for the integrity of the content of the paper
Competing interests: None declared