Cardiology in the Young

Brief Reports

Paroxysmal complete atrioventricular block in a patient with pulmonary atresia and intact ventricular septum

Akash R. Patela1 c1, David Goldberga1 and Maully Shaha1

a1 Division of Cardiology, Department of Pediatrics, The Children’s Hospital of Philadelphia, University of Pennsylvania School of Medicine, Pennsylvania, United States of America

Abstract

Sudden death in pulmonary atresia and intact ventricular septum with right ventricular dependent coronary circulation is a well-established complication, and is thought to be caused by myocardial ischaemia. We report a case of paroxysmal complete atrioventricular block that raises the possibility of an additional mechanism of sudden death.

(Received April 12 2010)

(Accepted August 21 2010)

(Online publication October 13 2010)