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Changing concepts of endocardial fibroelastosis

Published online by Cambridge University Press:  29 March 2010

Paul R. Lurie
Paul R. Lurie*
Affiliation:
Department of Pediatrics, Albany Medical College, New York, United States of America
*
Correspondence to: P. R. Lurie, Department of Pediatrics, Albany Medical College, 334 State Street, Albany NY, 12210, United States of America. Tel: +518 436 0903; E-mail: plurie1@verizon.net
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Abstract

Endocardial fibroelastosis is not a disease but a reaction of the endocardium. I review the history of the term with emphasis on the gradual understanding of the many causes of this reaction. I include a comprehensive list of diseases or other cardiac stresses that authors have reported in association, and I try to explain the mechanism of the reaction. Although endocardial fibroelastosis is rare today, I issue a warning of a possible epidemic recrudescence of some of the associated diseases. My hope is for nosologic purity, therefore that outworn but surviving concepts will be firmly rejected.

Keywords

Endocardial fibroelastosismechanismcardiomyopathy
Type
Review
Information
Cardiology in the Young , Volume 20 , Issue 2 , April 2010 , pp. 115 - 123
Copyright
Copyright © Cambridge University Press 2010

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