a1 Department of Otolaryngology, Westmead Hospital, University of Sydney, New South Wales, Australia
Objective: We report a case of Sweet's disease associated with rapid, profound loss of hearing, against a background of progressive, bilateral, sensorineural hearing loss.
Results: The clinical features were indistinguishable from those of immune-mediated inner ear disease. Establishment of a definitive diagnosis was a challenge due to the absence of a reliable diagnostic test. The patient was unresponsive to extensive immunosuppressive therapy and subsequently underwent cochlear implantation, with good hearing outcomes.
Conclusions: Profound, bilateral, sensorineural hearing loss in the context of Sweet's disease may be related to the underlying immunological aetiology. Cochlear implantation can successfully restore hearing when immunotherapy fails.
(Accepted May 19 2009)
(Online publication October 20 2009)
Dr S Cheng takes responsibility for the integrity of the content of the paper.
Competing interests: None declared