Intrahepatic right-to-left shunting after the Fontan operation
We describe two patients with right isomerism, corrected with a fenestrated Fontan operation, who suffered severe progressive cyanosis. Cardiac catheterisation in both revealed a massive right-to-left shunt from the inferior caval vein, through the liver, to a hepatic vein draining directly to the left side of the intra-atrial baffle. The anomalous vein was successfully ligated in both patients.(Published Online August 15 2006)
(Accepted January 23 2002)
Key Words: Congenital heart defects; isomerism; Fontan operation; cyanosis.
c1 Correspondence to: Marc R. de Leval, Cardiothoracic Unit, Great Ormond Street Hospital for Children NHS Trust, Great Ormond Street, London WC1N 3JH, UK. Tel: +44 20 7404 4383; Fax: +44 20 7831 4931; E-mail: DelevM@gosh.nhs.uk