Scimitar syndrome associated with absence of the right pulmonary artery and a persistent primitive hepatic venous plexus
An 18-month-old boy, referred because of an infection of the airways, was found to have a right-sided heart, a hypoplastic right lung, absence of the right pulmonary artery, and persistence of the hepatic venous plexus. The benign association of this unusual variant of the scimitar syndrome and persistence of the hepatic venous plexus needs to be recognised in order to avoid extensive investigations and surgery involving the inferior caval vein.(Accepted October 4 2004)
Key Words: Anomalous pulmonary venous connection; anomalous systemic venous connection; inferior caval vein.
c1 Correspondence to: Gabriella Agnoletti, Service de Cardiologie Pédiatrique, Groupe Hospitalier Necker-Enfants-Malades, 149, rue de Sèvres, 75743 Paris, France. Tel: +33 1 4449 4356; Fax: +33 1 4449 5724; E-mail: firstname.lastname@example.org