Cardiology in the Young

Brief Report

Cleft mitral valve in transposition with intact ventricular septum

Samuel Menahem a1c1 and Robert H. Anderson a2
a1 Department of Cardiology, Royal Children’s Hospital & Monash Medical Centre, Melbourne, Australia
a2 Institute of Child Health, Great Ormond Street Hospital, London, UK

Article author query
menahem s   [PubMed][Google Scholar] 
anderson rh   [PubMed][Google Scholar] 


We describe two cases of an isolated cleft of the mitral valve in transposition with intact ventricular septum. The cleft is positioned leftward in the pulmonary leaflet, at about 2 o’clock, when viewed from below looking at the cardiac short axis with the right ventricle to one’s left hand. Such clefts, when seen in the Taussig-Bing malformation are also positioned leftward.

In keeping with our current knowledge of cardiac development, our cases provide further evidence that transposition with an intact ventricular septum is the end-point of the Taussig-Bing spectrum.

(Accepted May 18 2004)

Key Words: Discordant ventriculo-arterial connections; Taussig-Bing malformation; trifoliate left atrioventricular valve.

c1 Correspondence to: Samuel Menahem, Murdoch Children’s Research Institute, Monash University Heart and Chest Research Institute, Royal Children’s Hospital, Flemington Road, Parkville, Vic 3052, Australia. Tel: +61 3 9345 5712; Fax: +61 3 9345 6001; E-mail: