Pulmonary atresia with intact ventricular septum and antenatal left ventricular failure
Pulmonary atresia with intact ventricular septum has been described extensively, and it is recognized that associated abnormalities of the coronary arteries may cause ischemia. We describe a fetus, diagnosed antenatally as having pulmonary atresia with intact ventricular septum and severe hypoplasia of the right ventricle, who developed severe left ventricular dysfunction. We hypothesize that this is due to reduced coronary blood flow because of falling right ventricular volume in the presence of complete right ventricular coronary arterial dependence.(Accepted December 22 2003)
Key Words: Pulmonary atresia; antenatal left heart failure.
c1 Correspondence to: Walter Duncan MD, Department of Pediatrics, Division of Cardiology, British Columbia Children's Hospital, 4480 Oak St., Vancouver, B.C. V6H 3V4, Canada. Tel: +1 604 875 2855; Fax: +1 604 875 3463; E-mail: firstname.lastname@example.org