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Superior semicircular canal dehiscence syndrome: a new aetiology

Published online by Cambridge University Press:  08 March 2017

P Puwanarajah ,
P Pretorius  and
I Bottrill
P Puwanarajah
Affiliation:
Department of Otolaryngology, John Radcliffe Hospital, Oxford, UK
P Pretorius
Affiliation:
Department of Neuroradiology, John Radcliffe Hospital, Oxford, UK
I Bottrill*
Affiliation:
Department of Otolaryngology, John Radcliffe Hospital, Oxford, UK
*
Address for correspondence: Mr I Bottrill, Consultant Otolaryngologist, Department of Otolaryngology, John Radcliffe Hospital, Oxford OX3 9DU, UK. E-mail: ian.bottrill@zen.co.uk
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Abstract

Objective:

We report what we believe to be a unique aetiology of the superior semicircular canal dehiscence syndrome, a recently described condition in which vestibular imbalance and/or hearing loss results from the loss of continuity of the bone overlying the superior semicircular canals.

Case report:

A 58-year-old woman presented with autophony in the right ear and momentary imbalance when shouting (Tullio phenomenon). Temporal bone computed tomography revealed a defect of the right superior semicircular canal caused by an enlarged superior petrosal sinus receiving drainage from a large cerebellar developmental venous anomaly.

Conclusions:

We review superior semicircular canal dehiscence syndrome and its management, and we discuss common aetiologies, contrasting these with the unusual aetiology presented here. We conclude that superior semicircular canal dehiscence syndrome may present with a solely developmental aetiology, despite presenting late in life.

Keywords

Semicircular CanalsPetrosal SinusVertigo
Type
Clinical Record
Information
The Journal of Laryngology & Otology , Volume 122 , Issue 7 , July 2008 , pp. 741 - 744
Copyright
Copyright © JLO (1984) Limited 2008

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