Cardiology in the Young
- Cardiology in the Young / Volume 9 / Issue 05 / September 1999, pp 512-515
- Copyright © Cambridge University Press 1999
- DOI: http://dx.doi.org/10.1017/S104795110000545X (About DOI), Published online: 19 August 2008
Brief Reports
Pulmonary atresia with intact ventricular septum, right-sided aortic arch, and an aorto-pulmonary collateral artery
Chandrakant R. Patela1 c1, Michael L. Spectora1 and Kenneth G. Zahkaa1
a1 Department of Pediatrics, Division of Pediatric Cardiology, and Department of Cardiothoracic Surgery, Rainbow Babies and Children's Hospital, Case Western Reserve University School of Medicine, Cleveland, OH, USA
Abstract
Described is a rare association in a patient with the heart in the left chest, namely pulmonary atresia with intact ventricular septum, fistulous coronary arterial connections, a right-sided aortic arch and an aorto-pulmonary collateral artery feeding one lung. The pulmonary arteries were non-confluent, with the right lung supplied by the right arterial duct originating from the under surface of the right-sided aortic arch, and the left lung supplied through the aorto-pulmonary collateral artery arising from the descending aorta. The surgical management is different in the setting of non-confluent pulmonary arteries.
(Accepted March 01 1999)
Keywords
Correspondence:
c1 Chandrakant R Patel, MBBS, Rainbow Babies and Childrens Hospital, Case Western Reserve University, 11100 Euclid Avenue, Cleveland, OH 44106, USA. Tel: +1 (216) 8443275; fax: +1 (216) 844478.
